Skoliose und Kyphose — idiopathisch, neuromuskulär, syndromal (Larsen, Parkinson). AIS, kombinierte Verfahren.
Ioan Branea
Center for Spine Surgery, Orthopedics, and Traumatology,
SRH Klinikum Karlsbad-Langensteinbach
Karlsbad, Germany
After ventral release – 20°
After ventral release and under Halo-traction
SRH Unternehmen – Max Mustermann
7
00.00.2020
After ventral release -20°
1 year postop
postop
1 year postop
postop
Anterior mobilisation with shortening of the anterior column results in a substantial correction of scoliosis
A nearly complete correction in frontal as well as in sagittal plane is possible even in severe rigid deformities
The sagittal profile improves with increasing kyphosis
Correction occurs spontaneously without application of corrective forces
- Conclusions –
Combined anterior-posterior approach
Ioan-Lucian Branea 1, Michael Ruf, Tobias Pitzen 2, Dezsö Jeszenszky 3, Iulian Tiripa 2
1. Rhein-Neckar Wirbelsäulenzentrum, St. Josefskrankenhaus, Heidelberg, Deutschland
2. Zentrum für Wirbelsäulenchirurgie, SRH Klinikum Karlsbad, Deutschland
3. Wirbelsäulenchirurgie, Schulthess Klinik, Zürich, Schweiz
Is a rare, autosomal dominant, congenital disorder first described by Larsen et al. 1950 (defect of Filamin-B encoding gene)
Features multiple dislocation of the great joints, flat facial shape, prominent foreheads and depressed nasal bridges, hypertelorism, brachydactyly
Other features may include short stature, hypermobility, cleft palate, hearing loss
3
Occur in 84% of individuals with Larsen syndrome, 50% are in the cervical spine*
No bony connection between dorsal and anterior elements, pedicles remain cartilaginous
Consequently: olisthesis, segmental kyphosis, neurological impairment…
Knowledge of the natural history, early diagnosis and adequate therapy is paramount!
*Johnston CE, 2nd, Birch JG, Daniels JL. Cervical kyphosis in patients who have Larsen syndrome. J Bone Joint Surg Am. 1996
retrospective analysis of 5 consecutive patients with C-spine anomalies whithin Larsen disease treated in Langensteinbach and Zürich (2012 – 2023)
predominant focal deformity was segmental kyphosis (2) and olisthesis(3)
neurological deficit was present in all patients
all 5 patients were preoperatively unable to walk due to progressive neurological deterioration and major joints subluxation
5
Mean age 17 years (2- 49 years), 2 ♀, 3 ♂
All received preoperative halo-gravity traction, followed by staged procedures with back/front or front/back decompression - fixation – fusion
4 cases received primary treatment, 1 case was a revision (after dorsal laminar wiring elsewhere)
Postoperative all improved neurologically, 3 patients regained their walking ability
Complications: screw – pullout in 1, plate-breakage in 1, both revised
postoperative after laminar wiring elsewhere
after 3 months marked kyphosis progression
after partiall removal of dorsal implants and halo-gravity traction
follow-up 7 years after
Sagital CT-reconstruction pre- and postop
♂, 49, preop MRI and x-ray
Postoperative images after halo-gravity traction, staged dorso-ventral decompression and fusion C2-T1. Patient regained walking ability
Postoperative result, patient regained ambulation
Postop MRI showing excellent cord decompression.
X-ray 1 year postop showing broken anterior plate
X-ray 8 year postop
Patients with Larsen syndrome should be screened for segmental kyphosis of the cervical spine and early neurological deficit
Fixation and fusion of the dorsal elements alone will most likely fail in kyphosis
We recommend dorsal fixation using pedicle screws
Larsen syndrome has an early indication for 360° decompression/ fixation/ fusion
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Finally, some time after leaving my previous workplace in Karlsbad-Langensteinbach, I have been able to resume my endeavours in adolescent scoliosis in Sankt-Josef Hospital in Heidelberg.
Ventral corection in idiopathic scoliosis has its classic indication in Lenke 1 and 5 type curves. Here are 2 interesting cases of „of the shelf“ use of anterior correction done recently:
First case - a 16 y.o. teenager with Lenke 6 curve measuring 87 degrees lumbar and 67 thoracic. He underwent a staged procedure with, at first, anterior derotating fusion of lumbar apex from T12 to L3. After the final dorsal correction operation both thoracic and lumbar curves were at 27 and 30 degrees, with a comparatively well balanced trunk.
I always dreaded inserting pedicle screws in a very rotated and laterally displaced lumbar apex such as this (especially in not skinny patients), on the other hand, from lateral, one is very close to the apical vertebral bodies.
The LIV is far from neutral, but fusing more distally would have compromised hopes of a good longterm result.
Second case – 16 y.o. girl with a Lenke 6 curve. Selective anterior fusion of the lumbar and thoracic apex led to decrease of the lumbar curve from 54 to 29 degrees and of the thoracic curve from 47 to 24 degrees by only fusing 1 (one!) lumbar and 5 thoracic segments. The „classic“ solution would have meant going dorsally from at least T4 to L3, even though a potential complete correction of the curves could have been achieved. Hybrid VBT would have been another , although also „unorthodox“, potential strategy.
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